Subcutaneous panniculitis–like T cell lymphoma in a patient with juvenile idiopathic arthritis treated with abatacept
نویسندگان
چکیده
A 35 year old female with JIA was diagnosed at eighteen months, initially oligoarticular, extending to a polyarticular pattern, with steroid dependent bilateral anterior uveitis necessitating immunosuppression. She received Abatacept infusions between December 2012 and July 2013. She had received numerous previous disease modifying agents including Sulfasalazine, Methotrexate, Hydroxychloroquine, Gold, Leflunamide, Adalimumab and Infliximab, which had been discontinued due to either intolerance or inefficacy.
منابع مشابه
Subcutaneous panniculitis-like T-cell lymphoma: Pediatric case series demonstrating heterogeneous presentation and option for watchful waiting.
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) and primary cutaneous gamma delta T-cell lymphoma (PCGD-TCL) were initially both classified as subcutaneous panniculitis-like T-cell lymphoma. In 2008, SPTCL with alpha-beta T-cell receptor subtype was separated from primary cutaneous gamma delta T-cell lymphomas (PCGD-TCL). We report four pediatric cases that demonstrate the heterogeneity ...
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